FBN1-Specific Polyclonal antibody

FBN1-Specific Polyclonal Antibody for IHC,ELISA

Host / Isotype

Rabbit / IgG

Reactivity

human, mouse, rat

Applications

IHC,ELISA

Conjugate

Unconjugated

Cat No : 20251-1-AP

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Synonyms

FBN, FBN1, fibrillin 1, MASS, MFS1, OCTD, SGS, WMS



产品信息

20251-1-AP targets FBN1-Specific in IHC, ELISA applications and shows reactivity with human, mouse, rat samples.

Tested Applications IHC,ELISA
Tested Reactivity human, mouse, rat
Immunogen Peptide 种属同源性预测
Host / Isotype Rabbit / IgG
Class Polyclonal
Type Antibody
Full Name fibrillin 1
Synonyms FBN, FBN1, fibrillin 1, MASS, MFS1, OCTD, SGS, WMS
Calculated Molecular Weight 312 kDa
GenBank Accession NumberNM_000138
Gene Symbol FBN1
Gene ID (NCBI) 2200
Conjugate Unconjugated
Form Liquid
Purification MethodAntigen affinity purification
UNIPROT IDP35555
Storage Buffer PBS with 0.02% sodium azide and 50% glycerol pH 7.3.
Storage ConditionsStore at -20°C. Stable for one year after shipment. Aliquoting is unnecessary for -20oC storage.

背景介绍

FBN1, also named as FBN, belongs to the fibrillin family. Fibrillins are structural components of 10-12 nm extracellular calcium-binding microfibrils, which occur either in association with elastin or in elastin-free bundles. Fibrillin-1-containing microfibrils provide long-term force bearing structural support. Defects in FBN1 are a cause of Marfan syndrome (MFS), isolated ectopia lentis (EL), Weill-Marchesani syndrome autosomal dominant (ADWMS), Shprintzen-Goldberg craniosynostosis syndrome (SGS) or MASS syndrome. This antibody is specific to FBN1.